Von Hippel-Lindau syndrome

Birt-Hogg-Dube syndrome

Hereditary papillary renal carcinoma

Hereditary leiomyomatosis and renal cell carcinoma syndrome

Succinate dehydrogenase-deficient tumor syndromes

BAP1 tumor predisposition syndrome

Hereditary pheochromocytoma-paraganglioma syndromes

Tuberous sclerosis

Genitourinary system and Lynch syndrome

Hereditary tumor syndromes associated with homologous recombination pathway mutations

Carney complex

Peutz-Jeghers syndrome

Mature B-cell lymphomas

Extranodal marginal zone lymphoma of MALT

Diffuse large B-cell lymphoma

Plasmacytoma

Histiocytic tumors

Juvenile xanthogranuloma

Mucosal melanoma

Fibroblastic and myofibroblastic tumors

The angiofibroma family of tumors

Solitary fibrous tumor

Inflammatory mrofibroblastic tumor

Vascular tumors

Hemangioma

Angiosarcoma

Pericytic (perivascular) tumors

Glomus tumor

Myointimoma

Myopericytoma

Extrarenal PEComa

Smooth muscle tumors

Leiomyoma

Leiomyosarcoma

Skeletal muscle tumors

Rhabdomyosarcoma

Tumors of uncertain differentiation

Synovial sarcoma

Extrarenal rhabdoid tumor

Desmoplastic small round cell tumor

Metastasis to the urinary tract

Metastasis to the kidney

Metastasis to the testis and paratestis

Neuroendocrine tumors

Well-differentiated neuroendocrine tumor

Neuroendocrine carcinomas

Small cell neuroendocrine carcinoma

Large cell neuroendocrine carcinoma

Mixed neuroendocrine neoplasms

Paragangliomas

Paragangliomas

Renal Cell Tumors

Clear Cell Renal Cell Tumors

Clear cell renal cell carcinoma

Multilocular cystic renal neoplasm of low malignant potential

Papillary Renal Tumors

Renal papillary adenoma

Papillary renal cell carcinoma

Oncocytic and Chromophobe Renal Tumors

Oncocytoma of Kidney

Chromophobe renal cell carcinoma

Other oncocytic tumors of kidney

Collecting Duct Tumors

Collecting duct carcinoma

Other renal tumors

Clear cell papillary renal cell tumor

Mucinous tubular and spindle cell carcinoma

Tubulocystic renal cell carcinoma

Acquired cystic disease-associated renal cell carcinoma

Eosinophilic solid and cystic renal cell carcinoma

Renal cell carcinoma NOS

Molecularly defined renal carcinomas

TFE3-rearranged renal cell carcinomas

TFEB-altered renal cell carcinomas

ELOC (formerly TCEB1) mutated renal cell carcinoma

Fumarate hydratase-deficient renal cell carcinoma

Succinate dehydrogenase deficient renal cell carcinoma

ALK-rearranged renal cell carcinoma

SMARCB1-deficient renal medullary carcinoma

Metanephric Tumors

Metanephric adenoma

Metanephric adenofibroma

Metanephric stromal tumor

Mixed epithelial and stromal renal tumors

Mixed epithelial and stromal tumor of the kidney

Pediatric cystic nephroma

Renal mesenchymal tumors

Adult renal mesenchymal tumors

Classic angiomyolipoma/PEComa of the kidney

Epithelioid angiomyolipoma/epithelioid PEComa of the kidney

Renal hemangioblastoma

Juxtaglomerular cell tumor

Renomedullary interstitial cell tumor

Pediatric renal mesenchymal tumors

Ossifying renal tumor of infancy

Congenital mesoblastic nephroma

Rhabdoid tumor of the kidney

Clear cell sarcoma of the kidney

Embryonal neoplasms of the kidney

Nephroblastic tumors

Nephrogenic rests

Cystic partially differentiated nephroblastoma

Nephroblastoma

Miscellaneous renal tumors

Germ cell tumors of the kidney

Benign and precursor squamous lesions

Condyloma acuminatum

Squamous cell carcinoma precursors, HPV-associated

Penile intraepithelial neoplasia, HPV-associated

Squamous cell carcinoma precursors, HPV-independent

Differentiated penile intraepithelial neoplasia, HPV-independent

Invasive epithelial tumors of the penis and scrotum

Invasive squamous epithelial tumors

HPV-associated squamous cell carcinoma

HPV-independent squamous cell carcinoma

Squamous cell carcinoma NOS

Other epithelial tumors

Penile adenosquamous and mucoepidermoid carcinomas

Extramammary Paget disease

Other scrotal tumors

Basal cell carcinoma of the scrotum

Epithelial tumors of the prostate

Glandular neoplasms of the prostate

Prostatic cysadenoma

High-grade prostatic intraepithelial neoplasia

Intraductal carcinoma of the prostate

Prostatic acinar adenocarcinoma

Prostatic ductal adenocarcinoma

Treatment-related neuroendocrine prostatic carcinoma

Squamous neoplasms of the prostate

Adenosquamous carcinoma of the prostate

Squamous cell carcinoma of the prostate

Adenoid cystic (basal cell) carcinoma of the prostate

Mesenchymal tumors unique to the prostate

Stromal tumors of the prostate

Prostatic stromal tumor of uncertain malignant potential

Prostatic stromal sarcoma

Epithelial tumors of the seminal vesicle

Glandular neoplasms of the seminal vesicle

Cystadenoma of the seminal vesicle

Adenocarcinoma of the seminal vesicle

Squamous neoplasms of the seminal vesicle

Squamous cell carcinoma of the seminal vesicle

Other tumors of the seminal vesicle

Mixed epithelial and stromal tumor of the seminal vesicle

Ovarian-type tumors of the collecting ducts and rete testis

Serous cystadenoma

Serous tumor of borderline malignancy

Serous cystadenocarcinoma

Mucinous cystadenoma

Mucinous borderline tumor

Mucinous cystadenocarcinoma

Endometrioid tumors

Clear cell adenocarcinoma

Brenner tumor

Tumors of the collecting ducts and rete testis

Adenoma of the collecting ducts and rete testis

Adenocarcinoma of the collecting ducts and rete testis

Paratesticular mesothelial tumors

Adenomatoid tumor

Well-differentiatied papillary mesothelial tumor

Mesothelioma

Tumors of the epididymis

Cystadenoma of the epididymis

Papillary cystadenoma of the epididymis

Adenocarcinoma of the epididymis

Squamous caell carcinoma of the epididymis

Melanotic neuroectodermal tumor of the epididymis

Germ cell tumors derived from germ cell neoplasia in situ

Non-invasive germ cell neoplasia

Germ cell neoplasia in situ

Specific forms of intratubular germ cell neoplasia

Gonadoblastoma

The germinoma family of tumors

Seminoma

Non-seminomatous germ cell tumors

Embryonal carcinoma

Yolk sac tumor, postpubertal-type

Choriocarcinoma

Placental site trophoblastic tumor

Epithelioid trophoblastic tumor

Cystic trophoblastic tumor

Teratoma, postpubertal-type

Teratoma with somatic-type malignancy

Mixed germ cell tumors of the testis

Mixed germ cell tumors

Germ cell tumors of unknown type

Regressed germ cell tumors

Germ cell tumors unrelated to germ cell neoplasia in situ

Spermatocytic tumor

Teratoma, prepubertal-type

Yolk sac tumor, prepubertal-type

Testicular neuroendocrine tumor, prepubertal-type

Mixed teratoma and yolk sac tumor, prepubertal-type

Sex cord stromal tumors of the testis

Leydig cell tumor

Leydig cell tumor

Sertoli cell tumors

Sertoli cell tumor

Large cell calcifying Sertoli cell tumor

Granulosa cell tumors

Adult granulosa cell tumor

Juvenile granulosa cell tumor

The fibroma thecoma family of tumors

Tumors in the fibroma thecoma group

Mixed and other sex cord stromal tumors

Mixed sex cord stromal tumor

Signet ring stromal tumor

Myoid gonadal stromal tumor

Sex cord stromal tumor NOS

Urothelial tumors

Non-invasive urothelial neoplasms

Urothelial papilloma

Inverted urothelial papilloma

Papillary urothelial neoplasm of low malignant potential

Non-invasive papillary urothelial carcinoma, low-grade

Non-invasive papillary urothelial carcinoma, high-grade

Urothelial carcinoma in situ

Invasive urothelial neoplasms

Invasive urothelial carcinoma

Squamous cell neoplasms of the urinary tract

Squamous papilloma of the urothelial tract

Squamous cell carcinomas of the urinary tract

Verrucous carcinoma of the bladder

Pure squamous carcinoma of the urothelial tract

Glandular neoplasms

Adenomas

Villous adenoma

Adenocarcinomas

Adenocarcinoma NOS

Urachal and diverticular neoplasms

Urachal carcinoma

Diverticular carcinoma

Urethral neoplasms

Urethral accessory gland carcinomas

Littre gland adenocarcinoma of the urethra

Skene gland adenocarcinoma of the urethra

Cowpwer gland adenocarcinoma of the urethra

Tumors of Mullerian type

Clear cell adenocarcinoma of the urinary tract

Endometrioid carcinoma of the urinary tract